Long QT Syndrome (LQTS)

About

• Long QT Syndrome (LQTS) is a condition affecting the electrical system of the heart, which increases the risk for an abnormally fast and chaotic heart rhythm. This abnormal heart rhythm can trigger a fainting spell, a seizure, or sudden cardiac death.
• Long QT syndrome an inherited condition, and can be triggered in some cases by exercise, a sudden loud noise, and certain medications that prolong the QT interval. There is also an ‘acquired’ Long QT syndrome caused by certain medications, electrolyte imbalances, or other medical conditions.
• Long QT syndrome is the most common of the genetic arrhythmia conditions and is treatable.
• Long QT syndrome is estimated to affect approximately 1 in 2,500 people of all ages, around the world. Most have Long QT type 1 or Long QT type 2, but there are several rarer types. A genetic test is used to determine the Long QT type.

Treatment/Standard of Care

Diagnosing Long QT syndrome includes looking at the clinical and family history, as well as cardiac testing. A normal ECG does not ‘rule out’ the diagnosis, and the standard recommendation is to see a cardiac specialist for evaluation.

Treatment includes medication, cardiac devices and avoiding other medications and conditions that can provoke an arrhythmia.

Additional Resources

Please note: The Canadian SADS Foundation provides links to external websites for informational purposes only. While we regard these as reputable sources of information, please be aware that The Canadian SADS Foundation is not responsible for the accuracy, legality, or content of the external site or for that of subsequent links.

Hear From Patients Living With Long QT Syndrome